McArdle's disease (glycogen storage disease type V) and anesthesia--a case report and review of the literature.
نویسنده
چکیده
McArdles disease (glycogen storage disease type v) is a rare condition in which energy-metabolism in the muscle is hampered. A case report is presented and the possible risk for perioperative complications including malignant hyperthermia is discussed. A checklist for the anesthesiological management of patients with McArdles disease is provided. A short overview of anesthesiological challenges and perioperative complications of other glycogen storage diseases is given.
منابع مشابه
McArdle's disease: case report and review of the literature.
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ورودعنوان ژورنال:
- Paediatric anaesthesia
دوره 23 9 شماره
صفحات -
تاریخ انتشار 2013